From: Cerebellar ataxia with sensory ganglionopathy; does autoimmunity have a role to play?
Subject | NCS Parameter | Median CMAP | Ulnar (ADM) CMAP | Tibial CMAP | Median SNAP | Ulnar SNAP | Radial SNAP | Sural SNAP | Superficial Peroneal SNAP | |||||
---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
Side | (R) | (R) | (R) | (R) | (L) | (R) | (L) | (R) | (L) | (R) | (L) | (R) | (L) | |
Patient 1 (Asymmetric SNAPs) 46Y, Female | Amplitude | 14.1 mV | 10.7 mV | 9.2 mV | 17.4 μV | 6.1 μV | 3.1 μV | 5.7 μV | 18.4 μV | 12.4 μV | 21.5 μV | 12.8 μV | 7.7 μV | 3.4. μV |
Conduction velocity | 60 m/s (Elbow-Wrist) | 60 m/s (Below elbow – Wrist) 70 m/s (Above elbow – below elbow) | NC | 56 m/s (Digit III –Wrist) | 60 m/s (Digit III –Wrist) | 58 m/s (Digit V –Wrist) | 57 m/s (Digit V–Wrist) | 58 m/s (Forearm- Snuff Box | 55 m/s Forearm- Snuff Box | 48 m/s Calf – lateral malleolus | 48 m/s Calf – lateral malleolus | 48 m/s Leg – Dorsum of the foot | 47 m/s Leg – Dorsum of the foot | |
Patient 2 (Absent SNAPS) 67Y, Male | Amplitude | 8.3 mV | 6.3 mV | 3.0 mV | NR | NR | NR | NR | NR | NR | NR | NR | NR | NR |
Conduction velocity | 54 m/s (Elbow-Wrist) | 48 m/s (Below elbow – Wrist) 59 m/s (Above elbow – below elbow) | NC | NA | NA | NA | NA | NA | NA | NA | NA | NA | NA |