| Details |
---|---|
Total number of patients | 50 |
Gender M/F | 27/23 |
Mean age [SD] at end of study in years (y) | 16.13 [5.5] |
Median age [min.-max.] at symptom/ sign onset (y) | 0.4 [0.00–8.5] |
Median age [min.-max.] at first clinical assessment (y) | 1.9 [0.3–16.3] |
Median age [min.-max.] at diagnosis of NF1 (y) | 2.2 [0.00–11.3] |
Mean age [SD] at last clinical assessment (y) | 13.6 [6.4] |
Mean duration [SD] of clinical follow up (y) | 10.1 [5.9] |
Total number of deaths | 4 |
Median age [min.-max.] at death (y) | 18.2 [2.3–28.1] |
Median maternal age {25th–75th %} and [min.-max.] at birth (y) | 27 {21–32}, [17–52] |