Table 2 Mortality in NF1 patients
Age at death (y) | Sex | Diagnosis |
|---|---|---|
2.3 | M | High grade pilomyxoid astrocytoma of the hypothalamus presenting with symptoms and signs of raised intracranial pressure |
13.0 | M | Disseminated metastatic high grade undifferentiated sarcoma with neuronal phenotype presenting with spinal cord compression |
23.4 | F | High grade malignant peripheral nerve sheath tumor presenting with cauda equina syndrome |
28.1 | M | Metastatic high grade spindle cell sarcoma arising from the pelvis and presenting with hematuria and bilateral hydronephrosis |