Fig. 2

Ultra widefield retinal imaging of the right retina. a Ultra-widefield color fundus image of the patient´s right eye showing atrophy of the optic nerve head (black arrow). b Ultra-widefield autofluorescent fundus image of the patient´s right eye showing loss of the normal hypofluorescence (darker signal) of the optic nerve (red arrow) due to loss of nerve fibers that leads to window-defect and hyperfluorescence from the underlying sclera. The rest of the ocular fundus shows normal autofluorescent signal, indicating a normal retinal pigment epithelium and photoreceptors. The inserts show corresponding color and autofluorescent findings in a normal, age-matched individual. The images of the left eye were corresponding (not shown here)