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Table 2 Cognitive disturbances in the spinocerebellar ataxias

From: Nonmotor symptoms in spinocerebellar ataxias (SCAs)

Cognitive disturbance

Spinocerebellar ataxia

Cognitive dysfunction

SCA1, 2, 3, 6, 7, 8, 10, 12, 17, 19, 21, DRPLA

Dementia (confirmed by specific testing)

SCA2, 8, 12, 17, 19, DRPLA

Mental retardation during childhood

SCA13

  1. SCA Spinocerebellar ataxia, DRPLA Dentatorubropalidoluisian atrophy